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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
61 %
Mots clés
Metabolism
Annexin A2
AAV vectors
AAV
Accelerometry
APOPTOSIS
Nuclear envelope
Muscle fibrosis
Omics
Fibrosis
Regeneration
Adipose tissue
Atrophy
Gene replacement
DNA methylation
Myoblasts
Myopathy
Cell therapy
Aggregate
Intercellular communication
Sarcopenia
Antiserum
Dystrophie musculaire oculopharyngée
Satellite cell
Haploinsufficiency
Pax7
OPMD
Regulatory T cells
Mass spectrometry
Dysferlinopathy
Pharyngeal muscle
Myosin
Myogenesis
AUTOPHAGY
Dysferlin
Myositis
PABPN1 agregates
Functional genomics
Actin
Andermann syndrome
Myopathies
Ageing
Triplet expansion disease
Effector T cells
Autologous
FAPs
Cross-bridge kinetics
Exon-skipping
Arbovirus
Neuromuscular disease
2-D PAGE
Differentiation
Gene therapy
Muscle strength
Amyotrophic Lateral Sclerosis
Antisens oligonucleotides
DUX4
Neuromuscular junction NMJ
Human
ALS
Myoblast
Xenograft
Anti-fibrotic pharmacotherapies
Satellite cells
GENE
RNA
FSHD
Anti-acetylcholine receptor antibodies
Muscle
Inflammation
Aged
Epigenetics
Skeletal muscle
Regenerative medicine
Transcriptomics
Muscle stem cells
Aav-U7
Biomarker
Alzheimer's disease
Dystrophin
Thérapie génique
Akt
MUTATIONS
Geriatric assessment
PABPN1
BINDING SPECIFICITY
Muscular dystrophy
Muscle dystrophy
DMD
Myotube
Oculopharyngeal muscular dystrophy
Alphavirus
Lamins
Duchenne muscular dystrophy
Agrégats de PABPN1
Autoimmune diseases
Bile salt hydrolases
AChR antibodies
Calcium
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